ICD-10-CM Code E75.3
Billable CodeBillable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis.
E75.3 is a billable ICD code used to specify a diagnosis of sphingolipidosis, unspecified. A 'billable code' is detailed enough to be used to specify a medical diagnosis.
The ICD code E753 is used to code Sphingolipidoses
Sphingolipidoses (singular "sphingolipidosis") are a class of lipid storage disorders relating to sphingolipid metabolism. The main members of this group are Niemann-Pick disease, Fabry disease, Krabbe disease, Gaucher disease, Tay-Sachs disease and Metachromatic leukodystrophy. They are generally inherited in an autosomal recessive fashion, but notably Fabry disease is X-linked recessive. Taken together, sphingolipidoses have an incidence of approximately 1 in 10,000, but substantially more in certain populations such as Ashkenazi Jews. Enzyme replacement therapy is available to treat mainly Fabry disease and Gaucher disease, and people with these types of sphingolipidoses may live well into adulthood. The other types are generally fatal by age 1 to 5 years for infantile forms, but progression may be mild for juvenile- or adult-onset forms.
|ICD 9 Code:||272.7|
Diagram showing some of the sphingolipidoses
- DRG Group #642 - Inborn and other disorders of metabolism.
ICD-10-CM Alphabetical Index References for 'E75.3 - Sphingolipidosis, unspecified'
The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code E75.3. Click on any term below to browse the alphabetical index.
Equivalent ICD-9 Code GENERAL EQUIVALENCE MAPPINGS (GEM)
This is the official approximate match mapping between ICD9 and ICD10, as provided by the General Equivalency mapping crosswalk. This means that while there is no exact mapping between this ICD10 code E75.3 and a single ICD9 code, 272.7 is an approximate match for comparison and conversion purposes.