ICD-10-CM Code E76.0
Mucopolysaccharidosis, type I
Non-Billable Code
Non-Billable means the code is not sufficient justification for admission to an acute care hospital when used a principal diagnosis. Use a child code to capture more detail.ICD Code E76.0 is a non-billable code. To code a diagnosis of this type, you must use one of the three child codes of E76.0 that describes the diagnosis 'mucopolysaccharidosis, type i' in more detail.
- E76.0 Mucopolysaccharidosis, type I NON-BILLABLE
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- BILLABLE E76.01 Hurler's syndrome
- BILLABLE E76.02 Hurler-Scheie syndrome
- BILLABLE E76.03 Scheie's syndrome
The ICD code E760 is used to code Hurler syndrome
Hurler syndrome, also known as mucopolysaccharidosis type I (MPS I), Hurler's disease, also gargoylism, is a genetic disorder that results in the buildup of glycosaminoglycans (formerly known as mucopolysaccharides) due to a deficiency of alpha-L iduronidase, an enzyme responsible for the degradation of mucopolysaccharides in lysosomes.:544 Without this enzyme, a buildup of heparan sulfate and dermatan sulfate occurs in the body. Symptoms appear during childhood and early death can occur due to organ damage.
| Specialty: | Endocrinology |
| MeSH Code: | D008059 |
| ICD 9 Code: | 277.5 |
ICD-10-CM Alphabetical Index References for 'E76.0 - Mucopolysaccharidosis, type I'
The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code E76.0. Click on any term below to browse the alphabetical index.
Parent Code: E76 - Disorders of glycosaminoglycan metabolism