ICD-10-CM Code E88.8
Other specified metabolic disorders
Non-Billable CodeNon-Billable means the code is not sufficient justification for admission to an acute care hospital when used a principal diagnosis. Use a child code to capture more detail.
ICD Code E88.8 is a non-billable code. To code a diagnosis of this type, you must use one of the two child codes of E88.8 that describes the diagnosis 'other specified metabolic disorders' in more detail.
- E88.8 Other specified metabolic disorders NON-BILLABLE
The ICD code E888 is used to code Trimethylaminuria
Trimethylaminuria (TMAU), as defined by the KIM consortium of endocrinology disorders as fish odor syndrome or fish malodor syndrome, is a rare metabolic disorder that causes a defect in the normal production of an enzyme named flavin-containing monooxygenase 3 (FMO3). When FMO3 is not working correctly or if not enough enzyme is produced, the body loses the ability to properly convert trimethylamine (TMA) from precursor compounds in food digestion into trimethylamine oxide (TMAO), through a process called N-oxygenation. Trimethylamine then builds up and is released in the person's sweat, urine, and breath, giving off a strong fishy odor or strong body odor. A variant of TMAU (secondary TMAU or TMAU2) exists where there is no genetic cause, yet excessive TMA is secreted, possibly due to intestinal dysbiosis, altered metabolism, or hormonal reasons.
|ICD 9 Code:||270.8|
Related Concepts SNOMET-CT
- Juvenile myopathy, encephalopathy, lactic acidosis AND stroke (disorder)
- Fukuhara syndrome (disorder)
- Liposynovitis prepatellaris (disorder)
- Hereditary benign acanthosis nigricans with insulin resistance (disorder)
- Infantile encephalopathy AND lactic acidosis (disorder)
ICD-10-CM Alphabetical Index References for 'E88.8 - Other specified metabolic disorders'
The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code E88.8. Click on any term below to browse the alphabetical index.