ICD-10-CM Code H49.819
Kearns-Sayre syndrome, unspecified eye
Billable CodeBillable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis.
H49.819 is a billable ICD code used to specify a diagnosis of kearns-Sayre syndrome, unspecified eye. A 'billable code' is detailed enough to be used to specify a medical diagnosis.
The ICD code H498 is used to code Kearns-Sayre syndrome
Kearns–Sayre syndrome (abbreviated KSS), also known as oculocraniosomatic disorder or oculocraniosomatic neuromuscular disorder with ragged red fibers, is a mitochondrial myopathy with a typical onset before 20 years of age. KSS is a more severe syndromic variant of chronic progressive external ophthalmoplegia (abbreviated CPEO), a syndrome that is characterized by isolated involvement of the muscles controlling movement of the eyelid (levator palpebrae, orbicularis oculi) and eye (extra-ocular muscles). This results in ptosis and ophthalmoplegia respectively. KSS involves a combination of the already described CPEO as well as bilateral pigmentary retinopathy and cardiac conduction abnormalities. Other symptoms may include cerebellar ataxia, proximal muscle weakness, deafness, diabetes mellitus, growth hormone deficiency, hypoparathyroidism, and other endocrinopathies. In both of these diseases, muscle involvement may begin unilaterally but always develops into a bilateral deficit, and the course is progressive. This discussion is limited specifically to the more severe and systemically involved variant.
|ICD 9 Code:||277.87|
- DRG Group #642 - Inborn and other disorders of metabolism.
Coding Advice SNOMET-CT
- Consider additional code to identify specific condition or disease
- Consider laterality specification
Equivalent ICD-9 Code GENERAL EQUIVALENCE MAPPINGS (GEM)
This is the official approximate match mapping between ICD9 and ICD10, as provided by the General Equivalency mapping crosswalk. This means that while there is no exact mapping between this ICD10 code H49.819 and a single ICD9 code, 277.87 is an approximate match for comparison and conversion purposes.