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ICD-10-CM Code Q40.0
Congenital hypertrophic pyloric stenosis

Billable Code
Billable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis.
POA Exempt
POA Exempt Code
The Center for Medicare & Medicaid Services (CMS) requires medical coders to indicate whether or not a condition was present at the time of admission, in order to properly assign MS-DRG codes. This "Present On Admission" (POA) indicator is recorded on CMS form 4010A.
| ICD-10 from 2011 - 2016

Q40.0 is a billable ICD code used to specify a diagnosis of congenital hypertrophic pyloric stenosis. A 'billable code' is detailed enough to be used to specify a medical diagnosis.

POA Indicators on CMS form 4010A are as follows:

IndicatorMeaningCMS Will Pay CC/MCC DRG Costs
YDiagnosis was present at time of inpatient admissionYes
NDiagnosis was not present at time of inpatient admissionNo
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.No
WClinically undetermined. Provider unable to clinically determine whether the condition was present at the time of inpatient admission.Yes
1Exempt from POA reportingNo

The ICD code Q400 is used to code Pyloric stenosis

Pyloric stenosis or pylorostenosis is narrowing (stenosis) of the opening from the stomach to the first part of the small intestine known as the duodenum, due to enlargement (hypertrophy) of the muscle surrounding this opening (the pylorus, meaning "gate"), which spasms when the stomach empties. This condition causes severe projectile non-bilious vomiting. It most often occurs in the first few months of life, when it may thus be more specifically labeled as infantile hypertrophic pyloric stenosis. The thickened pylorus is felt classically as an olive-shaped mass in the middle upper part or right upper quadrant of the infant's abdomen. In pyloric stenosis, it is uncertain whether there is a true congenital anatomic narrowing or whether there is merely a functional hypertrophy of the pyloric sphincter muscle. This condition typically develops in male babies in the first 2 to 6 weeks of life.

Specialty: General Surgery
MeSH Codes: D046248, D046248
ICD 9 Codes: 537.0, 750.5

Outline of stomach, showing its anatomical landmarks, including the pylorus.

Source: Wikipedia

Coding Notes for Q40.0 Info for medical coders on how to properly use this ICD-10 code

Inclusion Terms:
Inclusion Terms
Inclusion Terms are a list of concepts for which a specific code is used. The list of Inclusion Terms is useful for determining the correct code in some cases, but the list is not necessarily exhaustive.
Congenital or infantile constriction
Congenital or infantile hypertrophy
Congenital or infantile spasm
Congenital or infantile stenosis
Congenital or infantile stricture

MS-DRG Mapping

  • DRG Group #393-395 - Other digestive system diagnoses with MCC.
  • DRG Group #393-395 - Other digestive system diagnoses with CC.
  • DRG Group #393-395 - Other digestive system diagnoses without CC or MCC.

Related Concepts SNOMET-CT

  • Congenital pyloric spasm (disorder)
  • < 1.0 year
  • Age at onset of clinical finding (observable entity)


Congenital hypertrophic pyloric stenosis (exact match)

This is the official exact match mapping between ICD9 and ICD10, as provided by the General Equivalency mapping crosswalk. This means that in all cases where the ICD9 code 750.5 was previously used, Q40.0 is the appropriate modern ICD10 code.

Parent Code: Q40 - Other congenital malformations of upper alimentary tract

** This Document Provided By ICD.Codes **
Source: http://icd.codes/icd10cm/Q400