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ICD-10-CM Code Q87.0
Congenital malformation syndromes predominantly affecting facial appearance

Billable Code
Billable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis.
POA Exempt
POA Exempt Code
The Center for Medicare & Medicaid Services (CMS) requires medical coders to indicate whether or not a condition was present at the time of admission, in order to properly assign MS-DRG codes. This "Present On Admission" (POA) indicator is recorded on CMS form 4010A.
| ICD-10 from 2011 - 2016

Q87.0 is a billable ICD code used to specify a diagnosis of congenital malformation syndromes predominantly affecting facial appearance. A 'billable code' is detailed enough to be used to specify a medical diagnosis.

POA Indicators on CMS form 4010A are as follows:

IndicatorMeaningCMS Will Pay CC/MCC DRG Costs
YDiagnosis was present at time of inpatient admissionYes
NDiagnosis was not present at time of inpatient admissionNo
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.No
WClinically undetermined. Provider unable to clinically determine whether the condition was present at the time of inpatient admission.Yes
1Exempt from POA reportingNo

The ICD code Q870 is used to code Pierre Robin syndrome

Pierre Robin syndrome (abbreviated to PRS, and also known as Pierre Robin malformation, Pierre Robin anomaly or Pierre Robin anomalad) is a congenital condition of facial abnormalities in humans. PRS is a sequence, i.e. a chain of certain developmental malformations, one entailing the next. The three main features are cleft palate, retrognathia (abnormal positioning of the jaw or maxilla) and glossoptosis (airway obstruction caused by backwards displacement of the tongue base). A genetic cause to PRS was recently identified. Pierre Robin sequence may be caused by genetic anomalies at chromosomes 2, 11, or 17.

MeSH Codes: D010855, D054882, D000168, D006053, , , , , D000168,
ICD 9 Codes: 756.0, , 755.55, , , , , , 755.55,
Source: Wikipedia

Coding Notes for Q87.0 Info for medical coders on how to properly use this ICD-10 code

Inclusion Terms:
Inclusion Terms
Inclusion Terms are a list of concepts for which a specific code is used. The list of Inclusion Terms is useful for determining the correct code in some cases, but the list is not necessarily exhaustive.
Acrocephalosyndactyly [Apert]
Cryptophthalmos syndrome
Goldenhar syndrome
Moebius syndrome
Oro-facial-digital syndrome
Robin syndrome
Whistling face

MS-DRG Mapping

  • DRG Group #564-566 - Other musculoskeletal system and connective tissue diagnoses with MCC.
  • DRG Group #564-566 - Other musculoskeletal system and connective tissue diagnoses with CC.
  • DRG Group #564-566 - Other musculoskeletal system and connective tissue diagnoses without CC or MCC.

Related Concepts SNOMET-CT

  • Cryptophthalmos syndrome (disorder)
  • Aglossia-adactyly syndrome (disorder)

Coding Advice SNOMET-CT

  • Consider additional code to identify specific condition or disease

ICD-10-CM Alphabetical Index References for 'Q87.0 - Congenital malformation syndromes predominantly affecting facial appearance'

The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code Q87.0. Click on any term below to browse the alphabetical index.

Whistling face (Q87.0)
Ullrich-Feichtiger syndrome (Q87.0)
Robin(-Pierre) syndrome (Q87.0)
Papillon-Léage and Psaume syndrome (Q87.0)
Pierre Robin deformity or syndrome (Q87.0)
Marchesani(-Weill) syndrome (Q87.0)
Meyer-Schwickerath and Weyers syndrome (Q87.0)
Mohr's syndrome(Types I and II) (Q87.0)
Hallerman-Streiff syndrome (Q87.0)
Hanhart's syndrome (Q87.0)
Goldenhar(-Gorlin) syndrome (Q87.0)
Gorlin-Chaudry-Moss syndrome (Q87.0)
Fraser's syndrome (Q87.0)
Freeman Sheldon syndrome (Q87.0)
Dyscranio-pygo-phalangy (Q87.0)
Carpenter's syndrome (Q87.0)
Cyclopia, cyclops (Q87.0)
Cyclopism (Q87.0)
Acrocephalopolysyndactyly (Q87.0)
Acrocephalosyndactyly (Q87.0)
Aglossia-adactylia syndrome (Q87.0)


Acrocephalosyndactyly (approximate match)
Anomalies of skull and face bones (approximate match)

This is the official approximate match mapping between ICD9 and ICD10, as provided by the General Equivalency mapping crosswalk. This means that while there is no exact mapping between this ICD10 code Q87.0 and a single ICD9 code, 756.0 is an approximate match for comparison and conversion purposes.

Parent Code: Q87 - Other specified congenital malformation syndromes affecting multiple systems

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Source: http://icd.codes/icd10cm/Q870