ICD-10-CM Code H49.81
Non-Billable CodeNon-Billable means the code is not sufficient justification for admission to an acute care hospital when used a principal diagnosis. Use a child code to capture more detail.
ICD Code H49.81 is a non-billable code. To code a diagnosis of this type, you must use one of the four child codes of H49.81 that describes the diagnosis 'kearns-sayre syndrome' in more detail.
- H49.81 Kearns-Sayre syndrome NON-BILLABLE
The ICD code H498 is used to code Kearns-Sayre syndrome
Kearns–Sayre syndrome (abbreviated KSS), also known as oculocraniosomatic disorder or oculocraniosomatic neuromuscular disorder with ragged red fibers, is a mitochondrial myopathy with a typical onset before 20 years of age. KSS is a more severe syndromic variant of chronic progressive external ophthalmoplegia (abbreviated CPEO), a syndrome that is characterized by isolated involvement of the muscles controlling movement of the eyelid (levator palpebrae, orbicularis oculi) and eye (extra-ocular muscles). This results in ptosis and ophthalmoplegia respectively. KSS involves a combination of the already described CPEO as well as bilateral pigmentary retinopathy and cardiac conduction abnormalities. Other symptoms may include cerebellar ataxia, proximal muscle weakness, deafness, diabetes mellitus, growth hormone deficiency, hypoparathyroidism, and other endocrinopathies. In both of these diseases, muscle involvement may begin unilaterally but always develops into a bilateral deficit, and the course is progressive. This discussion is limited specifically to the more severe and systemically involved variant.
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Coding Notes for H49.81 Info for medical coders on how to properly use this ICD-10 code
Inclusion TermsInclusion Terms are a list of concepts for which a specific code is used. The list of Inclusion Terms is useful for determining the correct code in some cases, but the list is not necessarily exhaustive.
- Progressive external ophthalmoplegia with pigmentary retinopathy
Additional Code Note:
Use Additional CodeUse Additional Code note means a second code must be used in conjunction with this code. Codes with this note are Etiology codes and must be followed by a Manifestation code or codes.
- Code for other manifestation, such as:
- Heart block See code I45.9
ICD-10-CM Alphabetical Index References for 'H49.81 - Kearns-Sayre syndrome'
The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code H49.81. Click on any term below to browse the alphabetical index.