ICD-10-CM Code E76.02
Hurler-Scheie syndrome
Billable Code
Billable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis.E76.02 is a billable ICD code used to specify a diagnosis of hurler-Scheie syndrome. A 'billable code' is detailed enough to be used to specify a medical diagnosis.
The ICD code E760 is used to code Hurler syndrome
Hurler syndrome, also known as mucopolysaccharidosis type I (MPS I), Hurler's disease, also gargoylism, is a genetic disorder that results in the buildup of glycosaminoglycans (formerly known as mucopolysaccharides) due to a deficiency of alpha-L iduronidase, an enzyme responsible for the degradation of mucopolysaccharides in lysosomes.:544 Without this enzyme, a buildup of heparan sulfate and dermatan sulfate occurs in the body. Symptoms appear during childhood and early death can occur due to organ damage.
Specialty: | Endocrinology |
MeSH Code: | D008059 |
ICD 9 Code: | 277.5 |
MS-DRG Mapping
- DRG Group #642 - Inborn and other disorders of metabolism.
ICD-10-CM Alphabetical Index References for 'E76.02 - Hurler-Scheie syndrome'
The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code E76.02. Click on any term below to browse the alphabetical index.
Equivalent ICD-9 Code GENERAL EQUIVALENCE MAPPINGS (GEM)
This is the official approximate match mapping between ICD9 and ICD10, as provided by the General Equivalency mapping crosswalk. This means that while there is no exact mapping between this ICD10 code E76.02 and a single ICD9 code, 277.5 is an approximate match for comparison and conversion purposes.
Parent Code: E76.0 - Mucopolysaccharidosis, type I