ICD-10-CM Section E70-E88
Metabolic disorders
- E70 Disorders of aromatic amino-acid metabolism NON-BILLABLE
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- BILLABLE E70.0 Classical phenylketonuria
- BILLABLE E70.1 Other hyperphenylalaninemias
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- E70.20 Disorder of tyrosine metabolism, unspecified BILLABLE
- E70.21 Tyrosinemia BILLABLE
- E70.29 Other disorders of tyrosine metabolism BILLABLE
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- E70.30 Albinism, unspecified BILLABLE
- E70.31 Ocular albinism NON-BILLABLE
- E70.32 Oculocutaneous albinism NON-BILLABLE
- E70.33 Albinism with hematologic abnormality NON-BILLABLE
- E70.39 Other specified albinism BILLABLE
- BILLABLE E70.5 Disorders of tryptophan metabolism
- BILLABLE E70.8 Other disorders of aromatic amino-acid metabolism
- BILLABLE E70.9 Disorder of aromatic amino-acid metabolism, unspecified
- E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism NON-BILLABLE
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- BILLABLE E71.0 Maple-syrup-urine disease
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- E71.11 Branched-chain organic acidurias NON-BILLABLE
- E71.12 Disorders of propionate metabolism NON-BILLABLE
- E71.19 Other disorders of branched-chain amino-acid metabolism BILLABLE
- BILLABLE E71.2 Disorder of branched-chain amino-acid metabolism, unspecified
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- E71.50 Peroxisomal disorder, unspecified BILLABLE
- E71.51 Disorders of peroxisome biogenesis NON-BILLABLE
- E71.52 X-linked adrenoleukodystrophy NON-BILLABLE
- E71.53 Other group 2 peroxisomal disorders BILLABLE
- E71.54 Other peroxisomal disorders NON-BILLABLE
- E72 Other disorders of amino-acid metabolism NON-BILLABLE
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- E72.00 Disorders of amino-acid transport, unspecified BILLABLE
- E72.01 Cystinuria BILLABLE
- E72.02 Hartnup's disease BILLABLE
- E72.03 Lowe's syndrome BILLABLE
- E72.04 Cystinosis BILLABLE
- E72.09 Other disorders of amino-acid transport BILLABLE
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- E72.20 Disorder of urea cycle metabolism, unspecified BILLABLE
- E72.21 Argininemia BILLABLE
- E72.22 Arginosuccinic aciduria BILLABLE
- E72.23 Citrullinemia BILLABLE
- E72.29 Other disorders of urea cycle metabolism BILLABLE
- BILLABLE E72.3 Disorders of lysine and hydroxylysine metabolism
- BILLABLE E72.4 Disorders of ornithine metabolism
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- E72.50 Disorder of glycine metabolism, unspecified BILLABLE
- E72.51 Non-ketotic hyperglycinemia BILLABLE
- E72.52 Trimethylaminuria BILLABLE
- E72.53 Hyperoxaluria BILLABLE
- E72.59 Other disorders of glycine metabolism BILLABLE
- BILLABLE E72.8 Other specified disorders of amino-acid metabolism
- BILLABLE E72.9 Disorder of amino-acid metabolism, unspecified
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- E73 Lactose intolerance NON-BILLABLE
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- BILLABLE E73.0 Congenital lactase deficiency
- BILLABLE E73.1 Secondary lactase deficiency
- BILLABLE E73.8 Other lactose intolerance
- BILLABLE E73.9 Lactose intolerance, unspecified
- E74 Other disorders of carbohydrate metabolism NON-BILLABLE
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- E74.00 Glycogen storage disease, unspecified BILLABLE
- E74.01 von Gierke disease BILLABLE
- E74.02 Pompe disease BILLABLE
- E74.03 Cori disease BILLABLE
- E74.04 McArdle disease BILLABLE
- E74.09 Other glycogen storage disease BILLABLE
- BILLABLE E74.4 Disorders of pyruvate metabolism and gluconeogenesis
- BILLABLE E74.8 Other specified disorders of carbohydrate metabolism
- BILLABLE E74.9 Disorder of carbohydrate metabolism, unspecified
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- E75 Disorders of sphingolipid metabolism and other lipid storage disorders NON-BILLABLE
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- E75.00 GM2 gangliosidosis, unspecified BILLABLE
- E75.01 Sandhoff disease BILLABLE
- E75.02 Tay-Sachs disease BILLABLE
- E75.09 Other GM2 gangliosidosis BILLABLE
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- E75.10 Unspecified gangliosidosis BILLABLE
- E75.11 Mucolipidosis IV BILLABLE
- E75.19 Other gangliosidosis BILLABLE
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- E75.21 Fabry (-Anderson) disease BILLABLE
- E75.22 Gaucher disease BILLABLE
- E75.23 Krabbe disease BILLABLE
- E75.24 Niemann-Pick disease NON-BILLABLE
- E75.25 Metachromatic leukodystrophy BILLABLE
- E75.29 Other sphingolipidosis BILLABLE
- BILLABLE E75.3 Sphingolipidosis, unspecified
- BILLABLE E75.4 Neuronal ceroid lipofuscinosis
- BILLABLE E75.5 Other lipid storage disorders
- BILLABLE E75.6 Lipid storage disorder, unspecified
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- E76 Disorders of glycosaminoglycan metabolism NON-BILLABLE
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- E76.01 Hurler's syndrome BILLABLE
- E76.02 Hurler-Scheie syndrome BILLABLE
- E76.03 Scheie's syndrome BILLABLE
- BILLABLE E76.1 Mucopolysaccharidosis, type II
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- E76.21 Morquio mucopolysaccharidoses NON-BILLABLE
- E76.22 Sanfilippo mucopolysaccharidoses BILLABLE
- E76.29 Other mucopolysaccharidoses BILLABLE
- BILLABLE E76.3 Mucopolysaccharidosis, unspecified
- BILLABLE E76.8 Other disorders of glucosaminoglycan metabolism
- BILLABLE E76.9 Glucosaminoglycan metabolism disorder, unspecified
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- E77 Disorders of glycoprotein metabolism NON-BILLABLE
- E78 Disorders of lipoprotein metabolism and other lipidemias NON-BILLABLE
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- BILLABLE E78.0 Pure hypercholesterolemia
- BILLABLE E78.1 Pure hyperglyceridemia
- BILLABLE E78.2 Mixed hyperlipidemia
- BILLABLE E78.3 Hyperchylomicronemia
- BILLABLE E78.4 Other hyperlipidemia
- BILLABLE E78.5 Hyperlipidemia, unspecified
- BILLABLE E78.6 Lipoprotein deficiency
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- E78.81 Lipoid dermatoarthritis BILLABLE
- E78.89 Other lipoprotein metabolism disorders BILLABLE
- BILLABLE E78.9 Disorder of lipoprotein metabolism, unspecified
- E79 Disorders of purine and pyrimidine metabolism NON-BILLABLE
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- BILLABLE E79.0 Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
- BILLABLE E79.1 Lesch-Nyhan syndrome
- BILLABLE E79.2 Myoadenylate deaminase deficiency
- BILLABLE E79.8 Other disorders of purine and pyrimidine metabolism
- BILLABLE E79.9 Disorder of purine and pyrimidine metabolism, unspecified
- E80 Disorders of porphyrin and bilirubin metabolism NON-BILLABLE
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- BILLABLE E80.0 Hereditary erythropoietic porphyria
- BILLABLE E80.1 Porphyria cutanea tarda
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- E80.20 Unspecified porphyria BILLABLE
- E80.21 Acute intermittent (hepatic) porphyria BILLABLE
- E80.29 Other porphyria BILLABLE
- BILLABLE E80.3 Defects of catalase and peroxidase
- BILLABLE E80.4 Gilbert syndrome
- BILLABLE E80.5 Crigler-Najjar syndrome
- BILLABLE E80.6 Other disorders of bilirubin metabolism
- BILLABLE E80.7 Disorder of bilirubin metabolism, unspecified
- E83 Disorders of mineral metabolism NON-BILLABLE
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- E83.00 Disorder of copper metabolism, unspecified BILLABLE
- E83.01 Wilson's disease BILLABLE
- E83.09 Other disorders of copper metabolism BILLABLE
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- E83.10 Disorder of iron metabolism, unspecified BILLABLE
- E83.11 Hemochromatosis NON-BILLABLE
- E83.19 Other disorders of iron metabolism BILLABLE
- BILLABLE E83.2 Disorders of zinc metabolism
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- E83.40 Disorders of magnesium metabolism, unspecified BILLABLE
- E83.41 Hypermagnesemia BILLABLE
- E83.42 Hypomagnesemia BILLABLE
- E83.49 Other disorders of magnesium metabolism BILLABLE
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- E83.50 Unspecified disorder of calcium metabolism BILLABLE
- E83.51 Hypocalcemia BILLABLE
- E83.52 Hypercalcemia BILLABLE
- E83.59 Other disorders of calcium metabolism BILLABLE
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- E83.81 Hungry bone syndrome BILLABLE
- E83.89 Other disorders of mineral metabolism BILLABLE
- BILLABLE E83.9 Disorder of mineral metabolism, unspecified
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- E84 Cystic fibrosis NON-BILLABLE
- E85 Amyloidosis NON-BILLABLE
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- BILLABLE E85.0 Non-neuropathic heredofamilial amyloidosis
- BILLABLE E85.1 Neuropathic heredofamilial amyloidosis
- BILLABLE E85.2 Heredofamilial amyloidosis, unspecified
- BILLABLE E85.3 Secondary systemic amyloidosis
- BILLABLE E85.4 Organ-limited amyloidosis
- BILLABLE E85.8 Other amyloidosis
- BILLABLE E85.9 Amyloidosis, unspecified
- E86 Volume depletion NON-BILLABLE
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- BILLABLE E86.0 Dehydration
- BILLABLE E86.1 Hypovolemia
- BILLABLE E86.9 Volume depletion, unspecified
- E87 Other disorders of fluid, electrolyte and acid-base balance NON-BILLABLE
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- BILLABLE E87.0 Hyperosmolality and hypernatremia
- BILLABLE E87.1 Hypo-osmolality and hyponatremia
- BILLABLE E87.2 Acidosis
- BILLABLE E87.3 Alkalosis
- BILLABLE E87.4 Mixed disorder of acid-base balance
- BILLABLE E87.5 Hyperkalemia
- BILLABLE E87.6 Hypokalemia
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- E87.70 Fluid overload, unspecified BILLABLE
- E87.71 Transfusion associated circulatory overload BILLABLE
- E87.79 Other fluid overload BILLABLE
- BILLABLE E87.8 Other disorders of electrolyte and fluid balance, not elsewhere classified
- E88 Other and unspecified metabolic disorders NON-BILLABLE
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- BILLABLE E88.1 Lipodystrophy, not elsewhere classified
- BILLABLE E88.2 Lipomatosis, not elsewhere classified
- BILLABLE E88.3 Tumor lysis syndrome
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- E88.40 Mitochondrial metabolism disorder, unspecified BILLABLE
- E88.41 MELAS syndrome BILLABLE
- E88.42 MERRF syndrome BILLABLE
- E88.49 Other mitochondrial metabolism disorders BILLABLE
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- E88.81 Metabolic syndrome BILLABLE
- E88.89 Other specified metabolic disorders BILLABLE
- BILLABLE E88.9 Metabolic disorder, unspecified
Coding Notes for Section E70-E88
- Section Notes:
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, Section E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
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Section Type-1 Excludes:
Type-1 Excludes
Type-1 Excludes mean the conditions excluded are mutually exclusive and should never be coded together. Excludes 1 means "do not code here." - Transitory endocrine and metabolic disorders specific to newborn - instead, use Section P70-P74