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ICD-10-CM Code E75.4
Neuronal ceroid lipofuscinosis

Billable Code
Billable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis.
| ICD-10 from 2011 - 2016

E75.4 is a billable ICD code used to specify a diagnosis of neuronal ceroid lipofuscinosis. A 'billable code' is detailed enough to be used to specify a medical diagnosis.

The ICD code E754 is used to code Jansky-Bielschowsky disease

Jansky–Bielschowsky disease is a late-infantile form of neuronal ceroid lipofuscinosis associated with a deficiency in tripeptidyl peptidase I.

Specialty: Endocrinology
MeSH Codes: D009472, D009472, D009472
ICD 9 Codes: 330.1, 330.1, 330.1
Source: Wikipedia

Coding Notes for E75.4 Info for medical coders on how to properly use this ICD-10 code

Inclusion Terms:
Inclusion Terms
Inclusion Terms are a list of concepts for which a specific code is used. The list of Inclusion Terms is useful for determining the correct code in some cases, but the list is not necessarily exhaustive.
Batten disease
Bielschowsky-Jansky disease
Kufs disease
Spielmeyer-Vogt disease

MS-DRG Mapping

  • DRG Group #056-057 - Degenerative nervous system disorders with MCC.
  • DRG Group #056-057 - Degenerative nervous system disorders without MCC.

ICD-10-CM Alphabetical Index References for 'E75.4 - Neuronal ceroid lipofuscinosis'

The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code E75.4. Click on any term below to browse the alphabetical index.

Vogt-Spielmeyer amaurotic idiocy or disease (E75.4)
Spielmeyer-Vogt disease (E75.4)
Lipofuscinosis, neuronal(with ceroidosis) (E75.4)
Kufs' disease (E75.4)
Jansky-Bielschowsky amaurotic idiocy (E75.4)
Ceroid-lipofuscinosis, neuronal (E75.4)
Batten(-Mayou) disease (E75.4)
Bielschowsky(-Jansky) disease (E75.4)
Amaurotic idiocy(infantile) (juvenile) (late) (E75.4)


Cerebral lipidoses (approximate match)

This is the official approximate match mapping between ICD9 and ICD10, as provided by the General Equivalency mapping crosswalk. This means that while there is no exact mapping between this ICD10 code E75.4 and a single ICD9 code, 330.1 is an approximate match for comparison and conversion purposes.

Parent Code: E75 - Disorders of sphingolipid metabolism and other lipid storage disorders

** This Document Provided By ICD.Codes **
Source: http://icd.codes/icd10cm/E754