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ICD-10-CM Code E74.4
Disorders of pyruvate metabolism and gluconeogenesis

Billable Code
Billable codes are sufficient justification for admission to an acute care hospital when used a principal diagnosis.
| ICD-10 from 2011 - 2016

E74.4 is a billable ICD code used to specify a diagnosis of disorders of pyruvate metabolism and gluconeogenesis. A 'billable code' is detailed enough to be used to specify a medical diagnosis.

The ICD code E744 is used to code Pyruvate carboxylase deficiency

Pyruvate carboxylase deficiency is an inherited disorder that causes lactic acid and other potentially toxic compounds to accumulate in the blood. High levels of these substances can damage the body's organs and tissues, particularly in the nervous system. Pyruvate carboxylase deficiency is a rare condition, with an estimated incidence of 1 in 250,000 births worldwide. This disorder appears to be much more common in some Algonkian Indian tribes in eastern Canada.

Specialty: Endocrinology
MeSH Code: D015324
ICD 9 Code: 271.8

Oxaloacetate is the product of pyruvate carboxylase

Source: Wikipedia

Coding Notes for E74.4 Info for medical coders on how to properly use this ICD-10 code

Inclusion Terms:
Inclusion Terms
Inclusion Terms are a list of concepts for which a specific code is used. The list of Inclusion Terms is useful for determining the correct code in some cases, but the list is not necessarily exhaustive.
Deficiency of phosphoenolpyruvate carboxykinase
Deficiency of pyruvate carboxylase
Deficiency of pyruvate dehydrogenase
Code Type-1 Excludes:
Type-1 Excludes
Type-1 Excludes mean the conditions excluded are mutually exclusive and should never be coded together. Excludes 1 means "do not code here."
Disorders of pyruvate metabolism and gluconeogenesis with anemia - instead, use code D55.-
Leigh's syndrome - instead, use code G31.82

MS-DRG Mapping

  • DRG Group #642 - Inborn and other disorders of metabolism.

ICD-10-CM Alphabetical Index References for 'E74.4 - Disorders of pyruvate metabolism and gluconeogenesis'

The ICD-10-CM Alphabetical Index links the below-listed medical terms to the ICD code E74.4. Click on any term below to browse the alphabetical index.


Glycogenosis (approximate match)
Other specified disorders of carbohydrate transport and metabolism (approximate match)

This is the official approximate match mapping between ICD9 and ICD10, as provided by the General Equivalency mapping crosswalk. This means that while there is no exact mapping between this ICD10 code E74.4 and a single ICD9 code, 271.8 is an approximate match for comparison and conversion purposes.

Parent Code: E74 - Other disorders of carbohydrate metabolism

** This Document Provided By ICD.Codes **
Source: http://icd.codes/icd10cm/E744